Collection of rare hereditary non-inflammatory disorders of abnormal deposition of substances in the cornea.
Classification
International Classification of Corneal Dystrophies (IC3D) (2015):
Sub-classified by the anatomic location affected
- Epithelial/subepithelial CD:
- Epithelial basement membrane corneal dystrophy (EBMCD), aka map-finger-dot dystrophy, Cogan microcystic dystrophy, and anterior basement membrane dystrophy
- Meesmann corneal dystrophy (MECD) or juvenile epithelial corneal dystrophy
- Epithelial-stromal or Bowman’s CD:
- Reis-Bückler’s corneal dystrophy (RBCD)
- Thiel-Behnke corneal dystrophy (honeycomb dystrophy)
- Stromal CD:
- Macular corneal dystrophy (MCD)
- Granular corneal dystrophy (GCD)
- Lattice corneal dystrophy (LCD)
- Endothelial CD:
- Fuchs endothelial corneal dystrophy (FECD)
- Posterior polymorphous corneal dystrophy (PPCD)
- Congenital hereditary endothelial dystrophy (CHED)
- X-linked endothelial corneal dystrophy (XECD)